| Isolated Angiitis of the Central Nervous System |
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Seon Jin Ji1, Jin Young Choi1, Won Kyu Choi1, Jae Seung Yang1, Jong Soo Kim1, Myung Soon Kim2 |
1Department of Pediatrics, Wonju College of Medicine, Yonsei University, Wonju, Korea
2Department of Radiology, Wonju College of Medicine, Yonsei University, Wonju, Korea |
| 고립성 중추신경 혈관염 1례 |
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지선진1, 최진영1, 최원규1, 양재승1, 김종수1, 김명순2 |
1연세대학교 원주의과대학 소아과학교실
2연세대학교 원주의과대학 방사선과학교실 |
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| Abstract |
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Isolated angiitis of the central nervous system is a rare clinicopathologic entity characterized by vasculitis restricted to the vessels of the central nervous system without other apparent systemic vasculitis. It manifests headache, higher cortical dysfunction, focal neurologic dysfunction and cranial nerve palsies.
We experienced a case of isolated angiitis of the central nervous system in 6 year-old girl who was admitted to out unit because of headache, hemiparesis and altered consciousness. The laboratory test for blood, urine, and cerebrospinal fluid are all within normal ranges. There was no evidence of systemic vasculitis.
The contrast enhanced brain CT scan showed low densities along the left cerebellar hemisphere and posterior aspect of temporal lobe without enhancement, and left lateral internal carotid angiogram showed poorly contrast filling along the territory of left posterior cerebral artery due to narrowing or ischemic changes of the vessels. Axial T2WI(TR/TE, 2190/80) of magnetic resonance imaging showed multiple scattered high signal intensities at left pons with cerebellar hemisphere and diffuse high signal intensity along the left occipital lobe with enlarged surrounding gyral patterns, and axial T1WI(TR/TE, 665/25) showed intense gyral pattern contrast enhancement along the left occipital lobe. Steroid was tried with apparent benefit.
We report a case of isolated angiitis of central nervous system with review of literature. |
| Key Words:
Isolated angiitis of the central nervous system, Magnetic resonance imaging |
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