A Case of Pseudohypoaldosteronism |
In Nam Kang, Jong Won Lee, Jin Guen Bang, Du Bong Lee |
Department of Pediatrics, ST. Francisco`s General Hospital, Seoul, Korea |
가성 저알도스테론증 1례 |
강인남, 이종원, 방진건, 이두봉 |
방지거병원 소아과 |
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Abstract |
Psudohypoaldosteronism is a salt-wasting disease with unresponsiveness to mineralcorticoid and normal renal and adrenal function. Characteristic findings are severe hyponatremia, hyperkalemia and hyperaldosteronemia. We experienced a case of pseudohypoaldosteronism ina 1-day-old female who was presented with abdominal distension. Laboratory data showed hyponatrmia, hyperkalemia, elevation of plasma renin activity and aldosterone concentration and normal renal, adrenal function.
We reported a case of pseudohypoaldosteronism with brief review of related literatures. |
Key Words:
Pseudohypoaldosteronism, Mineralcorticoid unresponsiveness |
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