A Case of Pulmonary Artery Sling Associated with Tracheobroncheal Hypoplasia |
Yong Han Sun, Ho Sung Kim, Jung Il Noh, Jung Yun Cho, Yong Soo Yun |
Department of Pediatrics, Seoul National University College of Medicine, Seoul, Korea |
기관 저형성(Tracheal Hypoplasia)을 동반한 폐동맥 슬링(Pulmonary Artery Sling)1례 |
선용한, 김호성, 노정일, 최정연, 윤용수 |
서울대학교 의과대학 소아과학교실 |
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Abstract |
Pulmonary artery sling is a rare vascular anomaly wherein the left pulmonary artery arises from the right pulmonary artery and then traverses between the esophagus and the trachea toward the hilum of the left lung. Associated anomalies are common, particularly those of the tracheobronchial tree, which have been found in more than 50% of patients. Cardiovascular anomalies such as persistent left superior vena cava, atrial septal defect, ventricular septal defect, patent ductus arteriosus and aortic arch anomalies are also found not infrequently. We have experienced a 20 day-old female who had showed severe respiratory distress and cyanosis. She was diagnosed as pulmonary artery sling associated with tracheobronchial hypoplasia
by echocardiography, angiography, esophagography and bronchography. We report this case with related literature review. |
Key Words:
Pulmonary artery sling, Tracheobronchial hypoplasia |
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