| A Case of Intestinal Neuronal Dysplasia |
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Se Young Kim2, Yon Ho Choe2, Jeong Kee Seo2, In One Kim1, Chong Jai Kim1 |
1Department of Radiology, College of Medicine, Seoul National University, Seoul, Korea
2Department of pediatrics, College of Medicine, Seoul National University, Seoul, Korea |
| Intestinal Neuronal Dysplasia 1례 |
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김세영2, 최연호2, 서정기2, 김종재1, 김인원1 |
1서울대학교 의과대학 진단방사선학교실
2서울대학교 의과대학 소아과학교실 |
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| Abstract |
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Intestinal neuronal dysplasia(IND) is a disease characterized clinically by symptoms of
intestinal obstruction and pathologically by hyperplasia of the submucosal and myenteric plexuses
with formation of giant ganglia. Chronic intestinal pseudo-obstruction is a clinical diagnosis,
composed of myopathic form and neuropathic form, and normal intestinal histology. Intestinal
neuronal dysplasia is a neuropathic form of chronic intestinal pseudo-obstruction. The clinical
presentation and the course of IND is very variable.
We experienced a case of intestinal neuronal dysplasia in a 5 year-old boy who had suffered
from recurrent abdominal pain and vomiting for 3 years. Small bowel series showed multiple
intestinal dilatations and delayed excretion of contrast media. He underwent exploratory
laparotomy. However no mechanical causes for markedly dilated intestine were found and he
received loop ileostomy. However, he suffered from recurrent vomiting and abdominal pain. So,
he received repair-operaton. The pathology of surgical specimen showed hyperplasia of the
submucosal and myenteric plexuses with giant ganglia. We report this case with a brief review
of the related literatures. |
| Key Words:
Intestinal neuronal dysplasia, Chronic idiopathic intestinal pseudo-obstruction syndrome |
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