An Autopsy Case of Tracheal Agenesis Type 2 |
Hyun Joo Lee1, Eun Ae Park1, Seung Joo Lee1, Mi Jeong Kim2, Soon Hee Seong2 |
1Department of Pediatrics, College of Medicin, Ewha Womans University, Seoul, Korea 2Department of Pathology, College of Medicin, Ewha Womans University, Seoul, Korea |
기관 무발생증 2형 1례 |
이현주1, 박은애1, 이승주1, 김지정2, 성순희2 |
1이화여자대학교 의과대학 소아과학교실 2이화여자대학교 의과대학 해부병리학교실 |
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Abstract |
Tracheal agenesis is the rare and uniformly lethal anomaly that presents with severe
respiratory distress and aphonia after birth. In this anomaly, the trachea is usually absent and air is reaching the bronchi through a communication with the esophagus. The diagnosis should be suspected in a nowborn infant with respiratory distress whose intubation is difficult.
We report an autopy case of tracheal agenesis, type 2 in a female newborn infant: Complete tracheal agenesis with the fistula between the esophagus and the carina. Associated anomalies were bilobed right lung, Meckel's divericulum and ventricular septal defect. |
Key Words:
Respiratory distress, Bronchoesophageal fistula, Tracheal agenesis |
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