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A Case of Berry Syndrome associated with Syndactyly

Journal of the Korean Pediatric Society 1998;41(4):543-547.
Published online April 15, 1998.
A Case of Berry Syndrome associated with Syndactyly
Sang Chun Jung, Kyoung Sim Kim, Yong Wook Kim, Ki Bok Kim
Department of Pediatrics, Kwangju Christian Hospital, Kwangju, Korea
합지증을 동반한 Berry 증후군 1례
정상천, 김경심, 김용욱, 김기복
광주기독병원 소아과
Correspondence: 
Sang Chun Jung, Email: 1
Abstract
Berry syndrome is a rare association of congenital heart anomalies which consists of a distal aortopulmonary window with aortic origin of the right pulmonary artery and hypoplasia or interruption of the aortic arch. This defect can be corrected only by immediate surgical intervention, so accurate preoperative diagnosis and detailed anatomic depiction of this syndrome are important in prognosis. We experienced a case of Berry syndrome in an 8-day-old male, who had presented with multiple malformation such as syndactyly, high arched palate and brain hemorrhage. The diagnosis was made by two-dimensional echocardiography. The case is presented with a brief review of related literatures.
Key Words: Berry syndrome, Syndactyly, Two-dimensional echocardiography


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