A Case of Berry Syndrome associated with Syndactyly |
Sang Chun Jung, Kyoung Sim Kim, Yong Wook Kim, Ki Bok Kim |
Department of Pediatrics, Kwangju Christian Hospital, Kwangju, Korea |
합지증을 동반한 Berry 증후군 1례 |
정상천, 김경심, 김용욱, 김기복 |
광주기독병원 소아과 |
Correspondence:
Sang Chun Jung, Email: 1 |
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Abstract |
Berry syndrome is a rare association of congenital heart anomalies which consists of a distal
aortopulmonary window with aortic origin of the right pulmonary artery and hypoplasia or
interruption of the aortic arch. This defect can be corrected only by immediate surgical intervention,
so accurate preoperative diagnosis and detailed anatomic depiction of this syndrome are
important in prognosis. We experienced a case of Berry syndrome in an 8-day-old male, who had
presented with multiple malformation such as syndactyly, high arched palate and brain hemorrhage.
The diagnosis was made by two-dimensional echocardiography. The case is presented with
a brief review of related literatures. |
Key Words:
Berry syndrome, Syndactyly, Two-dimensional echocardiography |
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