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A Case of Congenital Self-Healing Reticulohistiocytosis

Journal of the Korean Pediatric Society 1998;41(10):1424-1429.
Published online October 15, 1998.
A Case of Congenital Self-Healing Reticulohistiocytosis
Taek Sun Kim1, Chang Wan Kim1, Eun Ryoung Kim1, You Mee Kang1, Kye Yong Song2
1Department of Pediatrics, Sung-Ae General Hospital, Seoul, Korea
2Department of Pathology, School of Medicine, Chung-Ang University, Seoul, Korea
선천성 자가치유성 세망조직구증식증 1례
김택선1, 김창완1, 김은령1, 강유미1, 송계용2
1성애병원 소아과
2중앙대학교 의과대학 병리학교실
Eun Ryoung Kim, Email: 1
Congenital self-healing reticulohistiocytosis(CSHR) is a rare variant of cutaneous reticulohistiocytosis. We report a newborn who had about 25 reddish brown papulonodular lesions on whole body at birth. No extracutaneous involvement was found. All skin lesions involuted within 4 months spontaneously. Biopsy of a skin lesion showed marked aggregated histiocytic infiltration with some eosinophils. S-100 protein and lysozyme were positive. Electron microscopy revealed numerous dense bodies, often with a myelin-like core and some Birbeck granules. We described a detailed clinical features of this case and reviewed the literatures.
Key Words: Congenital self healing reticulohistiocytosis, Langerhans cell, Birbeck granule, Laminated body

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