| A Case of Myositis Ossificans Progressiva |
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So Young Park, Su Jin Lee, Ji A Chung, Seung Joo Lee |
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Department of Pediatrics, College of Medicine, Ewha Womans University, Seoul, Korea |
| 진행성 화골성 근염(Myositis Ossificans Progressiva) 1례 |
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박소영, 이수진, 정지아, 이승주 |
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이화여자대학교 의과대학 소아과학교실 |
Correspondence:
So Young Park, Email: 1
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| Abstract |
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Myositis ossificans progressiva(MOP) is a rare, slow progressive autosomal dominant disorder that principally affects children under the age 10 years. It is characterized by progressive fibroblastic proliferation, and subsequent calcification and ossification of subcutaneous fat, muscles, tendons, aponeuroses and ligaments. The disorder is often associated with symmetrical malformations of the digits, especially microdactyly or adactyly of the thumbs and great toes. The disease usually leads to extensive immobility and eventual disability.
We experienced a case of MOP in a 2-year-old male child who showed multiple tender nodules on the left occipital, superior and inferior scapular, mid-back and upper buttock area and digital malformations and was treated with etidronate disodium. A brief review of related literatures is also presented. |
| Key Words:
Myositis ossificans progressiva, Digital malformations |
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