| Flexible Bronchoscopic Finding of Congenital Lobar Emphysema |
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Young Mee Seo1, Jung Yeon Shim1, Bong Seong Kim1, So Duk Lim2, Soo-Jong Hong1 |
1Department of Pediatrics, Asan Medical Center, Ulsan University
2Department of Diagnostic Pathology, Asan M edical Center, Ulsan University |
| 기관지 연화증에 의한 선천성 대엽성 폐기종 1례 |
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서영미1, 심정연1, 김봉성1, 임소덕2, 홍수종1 |
1울산대학교 의과대학 서울중앙병원 소아과
2울산대학교 의과대학 진단병리과 |
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| Abstract |
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Congenital lobar emphysema is a rare disease and a cause of respiratory distress in early infancy.
The most common location of pulmonary involvement is the left upper lobe. We diagnosed a case
of congenital lobar emphysema in a 5-month-old female infant, who had a complex heart disease
using flexible bronchoscopy. In spite of palliative heart surgery, respiratory difficulty and cyanosis
did not improve and weaning from artificial ventilation was not possible. Chest X-ray and CT
scan showed persistent hyperinflation in the left upper lobe. So, we performed flexible bronchoscopy.
The findings showed no cartilage and patent bronchus during inspiration, but complete
collapse during expiration due to a check valve effect in the left upper lobar bronchus. After
excision of the involved lobe, the patient improved from respiratory distress. The observed airway
patency during inspiration, and dynamic airway collapse on expiration suggest that bronchomalacia
contributed to lung overinflation in this case. |
| Key Words:
Congenital lobar emphysema, Flexible bronchoscopy, Bronchomalacia, Dynamic airway collapse |
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