Hemangioendothelioma Leading to Obstruction of the Left Main Bronchus in Infant |
Bong Seong Kim1, Jung Yeon Shim2, Seung Il Park3, Sung Hye Park4, Soo-Jong Hong1 |
1Departments of Pediatrics, Asan Medical Center, College of M edicine, Ulsan University, Seoul, Korea 2Department of Pediatrics, Kangbuk Samsung, H ospital, Sungkunkwan University School of M edicine, Seoul, Korea 3Departments of Chest Surgery, Asan M edical Center, College of M edicine, Ulsan University, Seoul, Korea 4Departments of Diagnostic Pathology, Asan Medical, College of Medicine, Ulsan University, Seoul, Korea |
영아에서 혈관내피종(hemangioendothelioma)에 의한 좌측 주기관지 폐색 1례 |
김봉성1, 심정연2, 박승일3, 박성혜4, 홍수종1 |
1울산대학교 의과대학 서울중앙병원 소아과 2성균관대학교 의과대학 강북삼성병원 소아과 3울산대학교 의과대학 서울중앙병원 흉부외과 4울산대학교 의과대학 서울중앙병원 진단병리과 |
Correspondence:
Soo-Jong Hong, Email: sjhong@www.amc.seoul.kr |
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Abstract |
Hemangioendothelioma is the most common vascular tumor in children, however hemangioendothelioma
occurring in the bronchus is very rare. We experienced a case of hemangioendothelioma
in the left main bronchus of an infant which was successfully removed by a sleeve resection.
Respiratory distress developed in a 3-month-old female infant with roentgenographic finding of
hyperinflation of the left lung. Chest CT and MRI revealed a highly vascular tumor extending
from the wall of the left main bronchus leading to hyperinflation by a check-valve mechanism.
Bronchoscopic finding showed left main bronchus obstruction due to a round, hypervascular
protruding mass. Lung scans showed markedly decreased perfusion in the left lung. At the age of
4 months, a sleeve of the left main bronchus was resected and end-to-end anastomosis
performed. The excised specimen contained a hemangioendothelioma measuring 1.5¡¿1.5cm. Anastomotic
site narrowing was observed on postoperative bronchoscopy, but ventilation of the left
lung remained relatively good. Perfusion of the left lung and respiratory distress symptom was
markedly improved 2 months later. Hemangioendothelioma must be considered as one of the
causes of bronchial obstruction during infancy. |
Key Words:
Hemangioendothelioma, Bronchial obstruction, Infant |
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