A Case of Sporadic Caffey`s Disease(Infantile Cortical Hyperostosis) Without Mandibular Involvement |
Byoung Lae Oh, Seung Woo Paik, Wan Seob Kim |
Department of Pediatrics, Presbyterian Medical Center, Chonju, Korea |
하악골을 침범하지 않고 산발적으로 발생한 Caffey`s Disease 1례 |
오병래, 백승우, 김완섭 |
전주예수병원 소아과 |
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Abstract |
Caffey`s disease(infantile cortical hyperostosis) is an uncommon benign and self limited disorder of unknown etiology, affecting the skeleton and its contiguous fasciae and muscles. Its occurrence in isolated cases or in multiple members in families suggests the existence of two different forms, namely a sporadic form and a familial form. The tibia is the predominant bone known to be affected in the familial form, while the mandible is mostly affected in the sporadic form. This benign and self-limited disorder has rarely late recurrence or persistence of symptoms with deformity. The patient in this case had immediate and complete resolution of her symptoms while receiving acetaminophen with no recurrent bone formation during treatment with antiinflammatory drugs. We describe sporadic, nonfamilial Caffey`s disease, affecting both radii and tibiae, but not involving the mandibular in a 4-month-old female infant. |
Key Words:
Caffey`s disease, Infantile cortical hyperostosis, Sporadic, Familial |
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