A Case of Protein Losing Enteropathy Associated with Henoch-Sch nlein Purpura |
Kee Dae Kim, Chang Whan Oh, Eun Young Lee, Jae Young Kim |
Department of Pediatrics, St. Benedict Hospital, Busan, Korea |
Henoch-Sch nlein 자반증에서 발생된 단백소실장증 1례 |
김기대, 오창환, 이은영, 김재영 |
성분도병원 소아과 |
Correspondence:
Jae Young Kim, Email: jykim9@korea.com |
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Abstract |
Henoch-Sch nlein purpura(HSP) is an IgA mediated immune complex vasculitic disease characterized by non-thrombocytic purpura, arthritis, gastrointestinal manifestations, and glomerulonephritis. HSP related glomerulonephritis induces hypoproteinemia and edema in some cases. Protein-losing enteropathy is another rare but known manifestation of HSP leading to hypoproteinemia and edema. We report a 6-year-old girl with HSP who showed edema caused by intestinal protein loss, evidenced by elevated fecal alpha 1 antitrypsin clearance. |
Key Words:
Henoch-Sch nlein purpura , Protein losing enteropathy |
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