| A case of tuberous sclerosis developing with subependymal giant-cell astrocytoma. |
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Young Chul Ahn1, Yong Suk Choi1, Pyoung Han Hwang2, Jung Soo Kim2 |
1Department of Pediatrics, Chungju LeeRha Hospital, Chungju, Korea
2Department of Pediatrics, College of Medicine, Chonbuk National University, Chonju, Korea |
| 거대세포 성상세포종이 동반된 결절성 경화증 |
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안영철1, 최용석1, 황평한2, 김정수2 |
1청주 리라병원 소아과
2전북대학교 의과대학 소아과학교실 |
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Received: 4 March 1991 • Accepted: 24 April 1991 |
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| Abstract |
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Subependymal giant-cell astrocytoma is a rare cerebral glioma that characteristically arises in the
wall of the lateral ventricle and presents as an intraventricular mass, causing hydrocephalus by
obstruction of the foramen of Monro. The tumor mainly occurs in patients with tuberous sclerosis and
is slow growing and well circumscribed, so that long survival after total surgical resection is often
achieved.
We experienced a cas^ of tuberous sclerosis in 9-year-old male patient who presented typical
clinical manifestations and subependymal giant-cell astrocytoma developing with tuberous sclerosis
were biologically benign.
Diagnosis was confirmed by brain CT, facil skin biopsy and tumor mass biopsy. We applied surgical
resection in order to remove the mass.
Tumor removal relieved attending symptoms and achieved survival without notable functional
impairment. Herein, we presented the case with a brief review of the related literatures. |
| Key Words:
Subependymal giant-cell astrocytoma, Tuberous Sclerosis |
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