A case of a variant of Pierre Robin syndrome -cerebrocostomandibular syndrome-. |
Hye Jin Lee1, Eun Jin Mun1, Ock Seung Jeong1, Son Sang Seo1, Jeong Ja Kang2 |
1Department of Pediatrics, Ilsin Christian Hospital, Pusan, Korea 2Department of Radiology, Ilsin Christian Hospital, Pusan, Korea |
Pierre Robin 증후군의 변형
- Cerebrocostomandibular Syndrome 1례 - |
이혜진1, 문은진1, 정옥승1, 서손상1, 강정자2 |
1일신기독병원 소아과 2일신기독병원 방사선과 |
Received: 25 February 1991 • Accepted: 29 March 1991 |
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Abstract |
We experienced a case of cerebrocostomandibular syndrome in newborn consisted of costal
deficiency, and micrognathia.
It is a variant of Pierre Robin syndrome, and cleft palate and glossoptosis are frequently present.
Respiratory difficulty due to rib dysplasia result in poor prognosis for survival.
Brief review of literature was made. |
Key Words:
Cerebrocostomandibular syndrome |
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