One Case of Recovery Phase of Aplastic Crisis in Hereditary Spherocytosis with Family History. |
Eun Kyung Won, Dong Hyeon Kim, Ho Seung, Chang Hee Choi |
Department of Pediatrics, Seoul Adventist Hospital, Seoul, Korea |
가족력을 가진 재생불량성 발증 회복기의
선천성 구상적혈구증 1례 * |
원은경, 김동현, 성호, 최창희 |
서울위생병원 소아과 |
Received: 4 May 1990 • Accepted: 12 July 1990 |
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Abstract |
We experienced a case of hereditary spherocytosis patient who was in a recovery phase of aplastic
crisis at the time of presentation. This was a 7 years old boy with complaints of pallor and intermit-
tent abdominal pain. Asymptomatic jaundice was also found in the patient's grandfather and two
maternal uncles. Patient’s mother had splenectomy due to hereditary spherocytosis.
Diagnosis was made by morphology, osmotic fragility test, autohemolysis test of peripheral blood,
and bone marrow examination.
Splenectomy, as a choice of treatment, was done and remarkable symptomatic improvement was
achieved. |
Key Words:
Hereditary spherocytosis, Aplastic crisis, Family history |
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