A Case of Lissencephaly with West Syndrome. |
Byoung Yul Lim, Ji Ho Song, Sa Jun Chung, Chang Il Ahn |
Department of Pediatrics, College of Medicine, Kyung Hee University, Seoul, Korea |
West 증후군을 동반한 Lissencephaly 1례 |
임병열, 송지호, 정사준, 안창일 |
경희대학교 의과대학 소아과학교실 |
Received: 12 May 1990 • Accepted: 24 July 1990 |
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Abstract |
Neuronal migrational disorders of the brain represent abnormalities in the formation of the
neocortex caused by faulty migration of the subependimal neuroblasts. Lissencephaly is a rare
congenital anomaly representing an arrest of brain development before the third or fourth month of
gestaional age.
The most common clinical findings were seizure, delayed development, failure to thrive and
hydrocephalus. The authors experienced a case of lissencephaly with West syndrome. Diagnosis was
made by the characteristic CT, MRI and EEG findings. |
Key Words:
Lissencephaly, West syndrome |
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