Treatment of Congenital Pulmonary Arteriovenous Fistula with Therapeutic Embolization in a Child. |
Byung Hee Kim1, Young Soo Chun1, Jin Soo Choi1, Jae Sook Ma1, Tai Ju Hwang1, Jae Kyu Kim2 |
1Department of Pediatrics, Chonnam University Medical School, Kwyangju, Korea 2Departmant of Radiology, Chonnam University Medical School, Kwyangju, Korea |
색전요법을 이용한 선천성 폐동정맥루 치험 례 |
김병희1, 전영수1, 최진수1, 마재숙1, 황태주1, 김재규2 |
1전남대학고 의과대학 소아과학교실 2전남대학교 의과대학 방사선과학교실 |
Received: 20 March 1990 • Accepted: 3 April 1990 |
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Abstract |
Congential pulmonary arteriovenous fistula is an uncommon malformation which has an abnormal
connection between the pulmonary capillary bed, in which venous blood in the pulmonary artery is
shunted through the fistula into the pulmonary vein without exposure to alveolar air, enters the left
heart, and results in systemic arterial unsaturation, polycythemia, cyanosis and clubbing.
Death often results from cerebral abscess and rupture of the malformation with massive hemor-
rhage. Therapeutic intervention is recommended for all symptomatic patients because of the risk of
those serious complications.
Treatment options include surgery and transcatheter obliteration with steel coils or detachable
balloons. Because of the rarity of the condition, many decisions are still emperical. Therapeutic
embolization has the adventages that multiple bilateral pulmonary arteriovenous malformations can
be occluded and also that the procedure can be repeated if necessary. Most experience of this
technique has been delivered in adults and older children.
A 4-year old child with congenital pulmonary arteriovenous fistula, who had cyanosis and
hemoptysis, was treated with embolization technique using steel coils. After the first therapeutic
embolization, significant improvement of arterial blood gas values with disappearance of cyanosis
was noted. However, 3 months later, cyanosis with significant arterial oxygen unsaturation was
reappered. Thus the second procedure was performed, and then the patient became free from
symptoms. During the subsequent 12 months follow up period, he had no symptoms or complications. |
Key Words:
Pulmonary arteriovenous fistula, Therapeutic embolization |
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