| A Case of Congenital Cystic Adenomatoid Malformation (Type1) of the Lung. |
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Dong Sik Kim1, Hwang Min Kim1, Jae Seung Yang1, Baek Keun Kim1, Jong Soo Kim1, Dong Hwan Shin2 |
1Department of Pediatrics, Yonsei University, Wonju College of Medicine
2Department of Pathology, Yonsei University, Wonju College of Medicine |
| 폐의 선천성 낭포성 유선종 기형 (Type 1) 1례 |
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김동식1, 김황민1, 양재승1, 임백근1, 김종수1, 신동환2 |
1연세대학교 원주의과대학 소아과학교실
2연세대학교 원주의과대학 병리학교실 |
Correspondence:
Dong Hwan Shin,
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Received: 15 January 1990 • Accepted: 23 March 1990 |
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| Abstract |
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A rare form of congenital cystic lung disease, characterized by the presence of one or usually
multiple interconnecting cyst, is called congenital cystic adenomatoid malformation of the lung. This
disease almost invariably presents either in live premature or stillborn infants, and death in those
infants bom alive usually occurs within a few hours of birth.
Infants with congenital cystic adenomatoid malformation usually have tachypnea, cyanosis, and
other forms of respiratory distress at or shortly after birth. These manifestations are related to
expansion of the cysts with resultant compression of the remaining normal lung.
We have experienced a case of cystic adenomatoid malformation (Type I) of the lung in 10 months
old female infant who had frequent upper respiratory tract infection and respiratory distress.
A brief review of the related literature is presented. |
| Key Words:
Congenital Cystic Adenomatoid Malformation, Congenital Cystic Lung Disease |
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