A Case of Central Dysplasia. |
Seong Kuk Seo, In Sook Kim, Soon Yol Hwang, Han Young Jeong, Sung Won Kim, Kil Hyun Kim |
Department of Pediatrics, St. Benedict Hospital Busan, Korea |
Central Dysplasia 1례 |
서성국, 김인숙, 황순열, 정한영, 김성원, 김길현 |
부산성분도병원 소아과 |
Received: 9 November 1987 • Accepted: 7 September 1988 |
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Abstract |
The central dysplasia is rare, congenital central hand anomaly which is usually associated with
other anomalies such as radial dysplasia, ulnar dysplasia, syndactyly, absent carpal, carpal fusion,
split foot, cleft palate, deafness, cataract, cyclopia, congenital nystagmus, fundal damage, anonychia,
imperforate anus and congenital heart disease.
The etiology is unknown, and the incidence of the typical split hand is one in 90,000 at birth. The
genetics of this abnormality is not clear.
We experienced a case of central dysplasia in 3 month of life female patient. Diagnosis was
confirmed by clinical features, physical examination and radiologic findings.
A brief review of related literature was made. |
Key Words:
Central dysplasia |
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