| A Case of Wilson Disease. |
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Cheol Soo Dan1, Sang Hoon Lee1, Woo Yeong Chung1, Soon Yong Lee1, Jong Eun Joo2, Hye Jae Cho2 |
1Department of Pediatrics, Inje Medical College, Ptisan Paik Hospital, Korea
2Department of Pathology, Seoul Paik Hospital |
| Wilson병 1례 |
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단철수1, 이상훈1, 정우영1, 이순용1, 주종은2, 조혜제2 |
1인제의대 부산백병원 소아과학교실
2서울백병원 병리과학교실 |
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Received: 16 March 1988 • Accepted: 2 June 1988 |
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| Abstract |
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We have experienced a case of Wilson disease manifesting chronic hepatitis.
The patient, 10-year-old boy, has shown elevated SGOT and SGPT levels since 5 years ago, but no
other specific symptoms of Wilson disease. His younger sister died of fulminant hepatitis (absence of
hepatitis A or B markers) at the age of eight.
The diagnosis was based on the characteristic laboratory data and the histologic findings of liver
tissue by the light and electron microscopy.
We have treated the patients with D-penicillamine and pyridoxine and the blood lerels of SGOT
and SGPT have been decreased down to normal level and the urinary copper excretion in 24 hours
has been decreased.
We presented this case and reviewed related literatures briefly. |
| Key Words:
Wilson disease, Chronic hepatitis |
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