A Case of Pulmonary Lymphangiectasis Associated with Chylothorax. |
Min Hee Kim1, Jae Kyoung Lee1, Oh Bae Chun1, Byoung Hoon Yoo1, Jae Hyung Yoo2 |
1Department of Pediatrics, College of Medicine, Chung Ang University, Seoul, Korea 2Department of Pathology, College of Medicine, Chung Ang University, Seoul, Korea |
유미 흉이 동반된 폐림프관 확장증 1례 |
김민희1, 이재경1, 전오배1, 유병훈1, 유재형2 |
1중앙대학교 의과대학 소아과학교실 2중앙대학교 의과대학 병리학교실 |
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Abstract |
Congenital pulmonary lymphangiectasis is a rare abnormality usually becoming manifest at birth
and almost invariably fatal in neonatal period or early infancy. Chylothorax is an infrequent
manifestation of this disease. We report a patient with pulmonary lymphangiectasis, 3 year old male,
who had been suffered from persistent respiratory distress since 7 days after birth, in whom the
diagnosis was suggested by the appearance of chylothorax and confirmed by open lung biopsy. He
died of pulmonary failure 4 months after discharge.
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Key Words:
Pulmonary lymphangiectasis , Chylothorax.
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