| A Case of Glanzmann's Thromboasthenia. |
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Hee Kyung Park, Kyung Hee Kim, Sang Man Shin, Sang Jhoo Lee |
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Dept, of Pediatrics, College of Medicine, Soon Cheon Hyang University |
| 혈소판 무력증 1례 |
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박희경, 김경희, 신상만, 이상주 |
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순천향대학 의과대학 소아과학교실 |
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| Abstract |
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Glanzmann’s Thromboasthenia is a rare autosomal recessive hemorrhagic disorder characterized
by chronic nonthrombocytopenic purpura, a prolonged bleeding time, and deficient or absent clot
retraction. The major underlying abnormality is defective first phase aggregation of platelets, which
are unresponsive to ADP in any concentration.
The authors experienced one case of Glanzmann’s Thromboasthenia in a 8 year 10 month old
female, who had frequent epistaxis and gingival bleeding. Platelets of patient showed complete
absence of aggregation in response to ADP, collagen and epinephrine.
The review of the literature was made briefly.
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| Key Words:
Thromboasthenia, Platelet aggregation.
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