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A Case of Blue Rubber Bleb Nevus Syndrome.

Journal of the Korean Pediatric Society 1986;29(12):1372-1376.
Published online December 31, 1986.
A Case of Blue Rubber Bleb Nevus Syndrome.
Kwang Soo Oh1, Soon Kook Choi1, San Ho Kim1, Bock Keun Kee1, Hyung Sun Sohn2, Seok Don Park2
1Department of Pediatrics, Won Kwang University School of Medicine, Iri、Korea
2Department of Dermatology, Won Kwang University School of Medicine, Iri、Korea
청색 고무 포말 모반 증후군 1례
오광수1, 최순국1, 김산호1, 기복근1, 손형선2, 박석돈2
1원광대학교 의과대학 소아과학교실
2원광대학교 의과대학 피부과학교실
Abstract
The Blue Rubber Bleb Nevus Syndrome is defined as rarely occuring hemangioma of the skin and gastrointestinal tract, with intestinal hemorrhage. Bean in 1958 gave the name Blue Rubber Bleb Nevus (BRBN) to a variant of bluish hemangiomas of the gastrointestinal tract which causes bleeding, which had been described for the first time by Gascoyen. We experienced a case of Blue Rubber Bleb Nevus Syndrome in a 2 month old male who was admitted to our Hospital because of pallor and multiple hemangiomas on the general body surface. This skin lesion had been present since birth and had grown progressively in size and numbers and turned into blue color, but some lesions regressed spontaneously. The histopathologic findings of red hemangioma revealed dilated vascular spaces containing erythrocytes in papillary dermis and many large, irregular, vascular spaces lined by single layer of endothelial cells in mid reticular dermis. The sweat glands were in close proximity to many of the vascular structures. The radiologic examination revealed numerous tiny- polypoid filling defect in small and large intestine suggesting hemangiomas. The review of literature was made briefly.
Key Words: Blue rubber bleb nevus syndrome, Hemangioma of the skin and gastrointestinal tract


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