A Case of Myelofibrosis. |
Ho Seong Yoo, Jin Heon Kim, Keun Chul Myung, Chang Soo Ra |
Department of Pediatrics, College of Medicine,Chosun University |
골수섬 유증 (myelofibrosis) 1례 |
유호성, 김진헌, 명근천, 라창수 |
조선대학교 의과대학 소아과학교실 |
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Abstract |
Myelofibrosis is characterized by fibrosis of bone marrow, leukoerythrobla stotic anemia
and extramedullary hematopoesis with varying degree of hepatosplenomegaly. Idiopathic
myelofibrosis is primarily a disease of the adult and is rare in the pediatric age group.
We experienced a case of idiopathic myelofibrosis in a 2 year 5 month old male who showed
severe anemia with abnormal forms of red blood cell (teardrops, ovalocytes), nucleated red cells,
huge splenomegaly and fibrosis of the bone marrow. We presented a case of idiopathic
myelofibrosis with brief review of the literatures.
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Key Words:
Idiopathic myelofibrosis. |
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