A Case of Klippel-Trenaunary-Weber Syndrome. |
Do Seung Lee, Dae Yong Hwang, Jeong Sick Min, Jae Sun Park |
Department of Pediatrics,Kosin Medical College, Gospel Hospital, Busan, Korea |
Klippel-Trenaunay-Weber Syndrome 의 1례 |
이도승, 황대영, 민정식, 박재선 |
고신의대 부속 복음병원 소아과 |
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Abstract |
We report a case of Klippel-Trenaunay-Weber Syndrome in a 12 years old boy who had
large port-wine hemangioma, soft tissue & bony hypertrophy and varicose veins on the lower
leg. On the skin lesion, there are several black papules & crops of skin colored eruptions which
were found out microscopically to be intraepidermal bleeding focuses & harmatomatous
change of squamous cells into sebaceous cells respectively. In our case, femoral angiography
showed no A-V fistula. A brief review of literatures was made.
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Key Words:
Port-Wine hemangioma, Soft tissue & bony hypertrophy, Varicose vein. |
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