A case of myelofibrosis. |
Hae Jung Cho, Keun Chull Choi, Chul Lee, Myong Ho Lee, Sook Ja Park |
1Department of Pediatrics Presbyterian Medical Center, Chonju, Korea 2Department of Clinical Pathology Presbyterian Medical Center, Chonju, Korea |
유아에서 발생한 골수섬유증 1 례 |
조혜정, 최근철, 이 철, 이명호, 박숙자 |
1전주예수병원 소아과 2전주예수병원 임상병리과 |
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Abstract |
The so called “Myelofibrosis” within the category of myeloproliferative disorders consists
of various degrees of leukoerythroblatosis, bone marrow fibrosis, and extramedullary hema-
topoiesis with hepatosplenomegaly.
Primary myelofibrosis occurs predominantly in adults and few in childhood. We experie-
nced one case of myelofibrosis, at 17 month old male patient.
He was admitted due to intermittent fever, pallor and abdominal distension. On admission,
hepatosplenomegaly, anemia and generalized petechia without jaundice was noticed.
Leukoerythroblastosis and tear-drop cells were seen in the peripheral blood smear. Bone
marrow finding was diagnosed as myelofibrosis.
He was discharged without specific treatment.
A Brief reviewof related literature is. also presented.
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Key Words:
Myelofibrosis |
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