| Two Cases of the Salts Losing Congenital Adrenal Hyperplasia. |
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Hee Ju Kim, Hyung Ro Moon |
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Dept, of Pediatrics, College of Medicine, Seoul National University |
| 鹽分損失型 先天性 副腎皮質 過形成症 2例 |
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金喜珠, 文炯魯 |
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서울大學校 醫科大學 小兒科學 敎室 |
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| Abstract |
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The authers experienced two cases of salt losing congenital adrenal hyperplasia. Case I was a 100 day old male infant, who had dehydration, failure to thrive, and diffusely pigmented skin. Very low plasma aldosterone and markedly increased urinary 17KS were observed. He had been, treated with daily DOCA injection and oral hydrocortisone, successfully. Case H was a 5 year and 6 month old boy, who had excessive salt craving & precocious
puberty. He had had frequent episodes of dehydration. Urinary 17 KS was markedly increased. He has bean treated with oral hydrocortisone alone without further salt losing episode. Both patients were considered to have complete 21-hydroxylase deficiency. Review of literature and reference on salt losing congenital adrenal hyperplasia was attempted
briefly.
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| Key Words:
Salt losing congenital adrenal hyperplasia |
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