A Case Of Di Guglielmo Syndrome. |
In Soon Park, Choong Rae Kim, Jae Seon Park, Young Jeon Kim |
Dept. of Pediatrics, Pusan Gospel Hospital, Korea. |
Di Guglielmo 증후군의 1례 |
박인순, 김충래, 박재선, 김영전 |
부산기독병원 소아과 |
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Abstract |
We have experienced a case of Di Guglielmo Syndrome in a 15 years old girl who had the cheif complaints of dizziness, gereral malaise and fine pustules around the nose. It is a systemic hemopathy characterized by abnormal proliferation of defective erythroid and myeloid cells and is a rare disease in childhood. The peripheral blood showed many rubriblasts, myeloblasts, metamyelocytes and bone marrow also showed atypical prorubricytes and bizzar multinucleated rubriblasts. Brief review of related literatures was made. |
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