| Two Cases of Peutz-Jeghers Syndrome. |
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Jun Hee Sul, Kee Choon Kim, Byung Soo Kim, No author name is english No author name is english |
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Department of Pediatrics, Yonsei University college of Medicine, Seoul, Korea. |
| Peutz-Jeghers 증후군 2 예 |
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설준희, 김기춘, 김병수, 한동관 |
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연세대학교 의과대학 소아과교실 |
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| Abstract |
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Familial association of gastrointestinal polyposis with mucocutaneous pigmentation was first reportde by Peutz in 1921. Following reemphsis by Jeghers in 1949, it became a definite clinical disease entity known as Peutz-Jeghers syndrome, which is rare disease with about 12cases reported in Korea. This was a report of our experience with two cases of Peutz-Jeghers syndrome, which were diagnosed in a 4 year old boy, who had mucocutaneous pigmentation and multiple polyposis in the whole gastrointestinal tract. Main complaints were abdominal pain and bloody stool in 2 cases. Only one case had familial history whose father had pigmentation on the left flank. |
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