Two Cases of Hereditary Spherocytosis

Hwang, H.O.; Choi, B.H.; Shin, M.J.; Kang, S.C.; Bai, J.S.

Case Report

Journal of the Korean Pediatric Society 1975;18(9):646-650.
Published online September 30, 1975.

Two Cases of Hereditary Spherocytosis

H.O. Hwang¹, B.H. Choi¹, M.J. Shin¹, S.C. Kang¹, J.S. Bai²

¹Department of Pediatrics, Seoul Red Cross Hospital
²Department of Surgery, Seoul Red Cross Hospital

遺傳性球狀赤血球症 2 例

황향옥^¹^, 최봉호^¹^, 신미자^¹^, 강석철^¹^, 배진선^²

^¹서울적십자병원 소아과
^²서울적십자병원 외과

Abstract

Two cases of hereditary spherocytosis in one family were presented. One case(case 1), 15 year old boy, had icteric sclera since the age of 6. He was diagnosed as hereditary spherocytosis by faifiily history, increased osmotic fragility, increased autdheinolysis negative direct and indirect Cooinbs’ test, and spherocytes in peripheral blood smear. Splenectomy was performed on him -On Aug. 21, 1974 successfully. The other case (case 2)，younger sister of case 1, was a 12 year old girl whose sclera had been icteric since the age of 6. Splenectomy was done oh her on Jan. 21, 1975 sufccessfully. Both were discharged in hestlthy condition and in good health without any complication until now.