Two Cases of Hereditary Spherocytosis |
H.O. Hwang1, B.H. Choi1, M.J. Shin1, S.C. Kang1, J.S. Bai2 |
1Department of Pediatrics, Seoul Red Cross Hospital 2Department of Surgery, Seoul Red Cross Hospital |
遺傳性 球狀赤血球症 2 例 |
황향옥1, 최봉호1, 신미자1, 강석철1, 배진선2 |
1서울적십자병원 소아과 2서울적십자병원 외과 |
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Abstract |
Two cases of hereditary spherocytosis in one family were presented. One case(case 1), 15 year old boy, had icteric sclera since the age of 6. He was diagnosed as hereditary spherocytosis by faifiily history, increased osmotic fragility, increased autdheinolysis negative direct and indirect Cooinbs’ test, and spherocytes in peripheral blood smear. Splenectomy was performed on him -On Aug. 21, 1974 successfully. The other case (case 2),younger sister of case 1, was a 12 year old girl whose sclera had been icteric since the age of 6. Splenectomy was done oh her on Jan. 21, 1975 sufccessfully. Both were discharged in hestlthy condition and in good health without any complication until now.
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