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Case Report
A Case of Multiple Juvenile Xanthogranuloma Involving Skin and Systemic Organs
So Yeon Lee, Yong Seok Jang, Min Sun Kim, Yun Jeong Yang, Myoung Ja Jung, Pyoung Han Hwang
Clin Exp Pediatr. 2004;47(2):227-230.   Published online February 15, 2004
Juvenile xanthogranuloma(JXG) is one of the most common non-Langerhans cell histiocytosis, benign histiocytic proliferative disorder. It typically presents as a solitary, benign, rapidly growing cutaneous tumor that may regress spontaneously. Most cutaneous lesions of JXG occur in the head and neck region of infants and young children. This disease is usually present with cutaneous lesion only; visceral involvement including the...
Original Article
A case of myelofibrosis with juvenile xanthogranuloma.
Jong Chan Kim, Hae Yong Lee, Hwang Min Kim, Baek Keun Lim, Jong Soo Kim, Young Hyuk Lee
Clin Exp Pediatr. 1991;34(6):869-876.   Published online June 30, 1991
Myelofibrrosis is characterized by anemia, leukoerythroblastosis, extramedullary hematopoiesis, hepatosplenomegaly, osteosclerosis and fibrosis of bone marrow. Idiopathc myelofibrosis is usually a disease of the adult and is rare in the pediatric age group. Juvenile xanthogranuloma is characterized by multiple papules on forehead and scalp. Lipid laden histiocytes and Touton giant cell are found in skin biopsy. We experienced a case of myelofibrosis with juvenile xanthogranuloma....
A Case of Juvenile Chronic Myelogenous Leukemia Associated with Juvenile Xanthogranuloma.
Eun Yong Lee, Jin Tae Kim, Young Sook Hong, Soon Kyun Kim, Hyun Keum Lee
Clin Exp Pediatr. 1987;30(11):1299-1304.   Published online November 30, 1987
We experienced a case of juvenile chronic myelogenous leukemia associated with juvenile xanthogranuloma and neurofibromatosis. This 1-year 6-month-old male patient had multipe cafg-au-lait spots, numerous nontender, yellowish, dome-shaped papules and nodules, hepatosplenomegaly, and pneumonia. Hematologic & bone marrow examinations, chromosomal study, and skin biopsy were performed for diagnosis. A brief review of the related literatures was added.