| A Case of Currino Triad |
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S.S. Park1, G.H. Lee1, H.S. Kim1, K.H. Kim1, H.S. Lee1, Y.S. Lee2 |
1Department of Pediatrics, Chung Ang Gil hospital, Incheon, Korea
2Department of Radiology, Chung Ang Gil hospital, Incheon, Korea |
| Currarino triad 1례 |
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박성신1, 이광훈1, 김희섭1, 김길현1, 이학수1, 이영석2 |
1중앙 길병원 소아과
2중앙 길병원 방사선과 |
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| Abstract |
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Currarino triad is a unique malformation complex of congenital caudal anormalies, including anorectal malformation (anal stenosis, anal ectopia, imperforated anus), sacral bony abnormality (scimitar or crescentic bony defect, malsegmentation) and presacral mass (meningocele, teratoma, enteric cyst or any combination of these).
This triad is familial in at least half of cases and the usual symptomatology is constipation due to anorectal stenosis. The embryogenesis is presumably due to abnormal separation of the neuroectoderm from the endoderm, so this triad is in the spectrum of the split notochord syndrome.
We report a case of Currarino triad in 5-month-old female patient who had chronic constipation and abdominal distention with brief review of the related literatures. |
| Key Words:
Currarino triad |
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