| A Case of Band Heterotopia |
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Sung Koo Kim, Young Jun Kim, Young Ah Lee, Ha Joo Choi, Woo Kap Chung |
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Department of Pediatrics, Hallym University Medical College, Seoul, Korea |
| Band Heterotopia 1례 |
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김성구, 김영준, 이영아, 최하주, 김성구 |
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한림대학교 의과대학 소아과학교실 |
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| Abstract |
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The “band heterotopia” or “double cortex” is a brain anomaly that is presumed to
result from a premature arrest of neuronal migration. Generalized disorders of neuronal
migration to the cerebral cortex have been recognized since the end of the 19th century.
Recently, development of neuroimaging technique, such as MRI, have permitted easy
diagnosis of generalized neuronal migration disorder. This syndrome is prevalent in
females. Most patients present with generalized or multifocal epilepsy, some mental
retardation, pyramidal signs and in some dysarthria. Full scales I.Q.s ranging from
severely low to normal have been reported. EEG investigations usually demonstrate
generalized spike-and-wave discharges or multifocal EEG abnormalities. Classic MRI
findings demonstrate a band of subcortical gray matter heterotopia underlying the cortical
mantle and separated from it by a thin rim of white mater. We report a 3 year old girl
who present a single episode of generalized tonic clonic seizure with fever. Her MRI
showed characteristic findings of band heterotopia. She has not been showed further
seizure attack. She is being follow up at OPD without medication. |
| Key Words:
Band heterotopia, Double cortex, Seizure |
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