A Case of Melkersson-Rosenthal Syndrome |
Dae Hun Pee1, Yo Won Na1, Ki Young Chang1, Woo Keun Seo2, Kee Hyoung Lee1, Baik-Lin Eun1 |
1Department of Pediatrics, College of Medicine, Korea University, Seoul, Korea 2Department of Neurology, College of Medicine, Korea University, Seoul, Korea |
Melkersson-Rosenthal 증후군 1례 |
피대훈1, 나요원1, 장기영1, 서우근2, 이기형1, 은백린1 |
1고려대학교 의과대학 소아과학교실 2고려대학교 의과대학 신경과학교실 |
Correspondence:
Baik-Lin Eun, Email: bleun@chollian.net |
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Abstract |
Melkersson-Rosenthal syndrome(MRS) is a rare disorder, having a symptom triad of recurrent facial
palsy, orofacial swelling and fissured tongue(lingua plicata). This disorder is usually recurrent
or progressive, and monosymptomatic or oligosymptomatic forms have been reported to be more
common than classic forms. Generally, MRS occurs in young adults at the end of the second
decade of life and incidence of the disease in childhood is known to be very low. Although the
clinical manifestation of MRS in children is similar to that in adults, early diagnosis and management
is essential to avoid long-lasting functional disorders and psychological problems. We experienced
MRS in a 13 year old boy with a history of recurrent facial palsy. We report this case
with review of related literature. |
Key Words:
Melkersson-Rosenthal Syndrome |
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