A case of testicular adrenal rest tumor in a
male child with congenital adrenal hyperplasia |
Joo Hwa Kim, Kyong Ah Yun, Choong Ho Shin, Sei Won Yang |
Department of Pediatrics, College of Medicine, Seoul National University, Seoul, Korea |
선천 부신 과다형성 환자에서 발생한 고환 부신 잔류 종양 1례 |
김주화, 윤경아, 신충호, 양세원 |
서울대학교 의과대학 소아과학교실 |
Correspondence:
Choong Ho Shin, Email: chshinpd@snu.ac.kr |
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Abstract |
Testicular adrenal rest tumors are a well-known complication in male patients with congenital adrenal hyperplasia. Corticosteroid suppressive therapy usually results in the regression of these tumors. We describe a patient with 21-hydroxylase deficiency who developed bilateral testicular masses. Despite steroid suppressive therapy, the tumors did not regress and hormonal control was poor. Consequently, bilateral partial orchiectomies were performed. |
Key Words:
Testicular neoplasms, Adrenal rest tumor, Child, Congenital adrenal hyperplasia, Steroid, 21-hydroxy |
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