2 Case of Scimitar syndrome. |
Jae Kon Ko1, Nam Su Kim1, Woong Heum Kim1, Heung Jae Lee1, Shi Joon Yoo2 |
1Department of Pediatrics, Sejong General Hospital 2Department of Radiology, Sejong General Hospital |
Scimitar 증후군 2례 |
고재곤1, 김남수1, 김웅흠1, 이흥재1, 유시준2 |
1부천 세종병원 소아과 2부천 세종병원 방사선과 |
Received: 9 June 1989 • Accepted: 10 September 1989 |
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Abstract |
The scimitar syndrome, a rare complex anomaly, consists essentially of an anomalous pulmonary
vein draining whole or part of right lung into inferior vena cava and its curved Turkish sword
(scimitar) like appearance has provided the name of this syndrome.
Associated anomalies are frequent, such as hypoplasia of the right lung and right pulmonary artery,
abnormalities of bronchial architecture and lobation, rightward displacement of heart and systemic
arterial supply to the right lung.
Other congenital cardiac abnormalities are associated with about 25% of this syndrome.
We have experienced 2 cases of the scimitar syndrome in infant and 12year old boy recently, so we
presented with a brief review of the literatures. |
Key Words:
Scimitar syndrome |
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