A Case of Potter Syndrome with Bilateral Polycystic Kidneys. |
Chun Hwa Lee1, Jung Hwan Choi1, Yong Choi1, Chong Ku Yun1, Yeon Lim Suh2, Je G Chi2, Son Moon Shin3 |
1Department of Pediatrics, College of Medicine, Seoul- National University 2Department of Pathology, College of Medicine, Seoul- National University 3Department of Pediatrics, College of Medicine, Young Nam Univerity |
양측성 다발성 신낭종을 동반한 Potter 증후군 1례 |
이준화1, 최중환1, 최 용1, 윤종구1, 서연림2, 지제근2, 신손문3 |
1서울대학교 의과대학 소아과학교실 2서울대학교 의과대학 병리학 교실 3영남대학교 의과대학 소아과학교실 |
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Abstract |
In 1946, Potter described a series of 20 cases of infants in whom bilateral absence of the kidneys was
associated with hypoplasia of the lungs and characteristic faces.
Afterwards it has been known that any condition that causes significant reduction in urine formation or excretion will result in oligohydramnios accounts for many of the nonrenal features of Potter
syndorme. We report a case of Potter syndrome with bilateral polycystic renal dysplasia and add a brief
review of literatures.
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Key Words:
Potter syndrome, Oligohydramnios, Hypoplastic lung, Polycystic renal dysplasia.
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