A Case of Potter Syndrome. |
Young Mi Hong, Hae Seung Kim, Jung Gon Kim, Keun Lee |
Department of Pediatrics, College of Medicine,Ewha Womans University |
Potter 증후군의 1례 |
홍영미, 김혜승, 김중곤, 이 근 |
이화여자대학교 의과대학 소아과학교실 |
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Abstract |
In 1946 Potter described a series of 20 cases in infants in whom bilateral absence of the
kidneys was associated with, hypoplasia of the lung and characteristic face. The main facial
features she described were increased space between the eyes, a prominent fold which arises
at inner canthus and sweeps downward and laterally below the eyes, unusual flattening of the
nose, excessive recession of the chin, moderate enlargement and decreased chondrification of
the ear, and suggestion of premature senility.
We reported a female neonate diagnosed by autopsy as Potter syndrome which was
characterized by bilateral renal agenesis, bilateral pneumothorax and characteristic face.
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Key Words:
Potter syndrome, pneumothorax, renal agenesis |
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