A cases of Congenital Nephrogenic Diabetes Insipidus with Bilateral Hydronprosis. |
Young Mo Sohn, Chul Lee, Pyung Kil Kim, Duk Jin Yun |
Department of Pediatrics, College of Medicize Yonsei University Seoul, Korea. |
양측성 수신증이 동반된 선천성 신성뇨붕증 1례(Indomethacin 으로 치료한 1예)
|
손영모, 이 철, 김병길, 윤덕진 |
연세대학교 의과대학 소아과학교실 |
|
|
Abstract |
A 13 year old boy was diagnosed as primary nephrotic diabetesinsipidus, whose symptom has been devloped from 3 years of age, subsequetly he developed bilateral hydronephrosis and neurogenic bladder. His pedigree could be explored 5 generations and represented inheritace as X-linked recesslive transmission, He was treated with indomethacin 2mg/Kg/day plus chlorothiazid 500mg/dau and this new method shows markedly decreased urine outpur and increased urine osmolarity. |
|