| A Case Report of the Letterer-Siwe Disease |
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Y.J. Choi1, S.W. Ahn1, E.S. Chang1, K.P. Choi2, Y.K. Chun2, M.H. Huh3 |
1Dept. of Pediatrics Wallace Memorial Baptist Hospital, Pusan, Korea
2Dept. of Surgery Wallace Memorial Baptist Hospital, Pusan, Korea
3Dept.of Pathology Wallace Memorial Baptist Hospital, Pusan, Korea |
| —Lefferer-Siwe 씨 병 의 1 예 보고— |
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최영자1, 안소원1, 장응실1, 최건필2, 전열경2, 허만하3 |
1부산침례병원 소아과
2부산침례병원 의과
3부산침례병원 병리과 |
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| Abstract |
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A case of Letterer-Siwe disease in 1 4/12 year old boy manifesting all of the classic signs described by Siwe-hepatosplenomegaly, swelling of the lymph nodes, bleeding tendency, hypochromic anemia, fever and osseous lesions is presented. The diagnosis was confirmed by skin and lymph node biopsies and radiological evidence of bony defects in the skull and vertebrae. Brief review and discussion were made mainly on etiological factors, secondary infections, skin rashes and other clinical signs, and histological findings. This is the second reported case in Korean literature and the first one with histological confirmation on lymph node biopsy with specific bone
lesions.
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