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Case Report
A Case Report Kostmann Syndrome.
Han Wook Yoo, Son Moon Shin, Hyo Seop Ahn, Yong Choi, Chang Yee Hong
Clin Exp Pediatr. 1983;26(3):284-288.   Published online March 31, 1983
Kostmann syndrome (Infantile genetic agranulocytosis), a disease characterized by recurrent infections leading to death in infancy, shows an agranulocytosis with variable monocytosis, eosinophilia in the peripheral blood, accompanied by the maturation arrest of the myelocytic series at the promyelocyte-myelocyte level. A 2 years 3 month old female patient with Kostmann syndrome is reported, who has suffered from recurrent infections since 1 month of age. During...
Two Case of Ginaotti-Crosti Syndrome.
Jae Ho Lee, Soon Ung Kang, Jeong Kee Seo, Hyo Seop Ahn, Kwng Wook Ko, Won Suk Kim
Clin Exp Pediatr. 1982;25(12):1289-1294.   Published online December 31, 1982
The Gianotti-Crosti syndrome is an. infrequently recognized disorder with distinctive clinical features. We have experienced two cases of Gianotti-Crosti syndrome diagnosed by clinical manifestation, laboratory data and histopathologic finding of skin. Case one; An 18-month-old girl was admitted to the pediatric ward with the chief complaint of erythematous rash. Its onset was preceded by an. upper respiratory tract infection. She had a wide spread erythematous...
A Case of Acardi's Syndrome.
Bok Lyun Park, Hee Jung Chung, Chang Joon Coe, Young Sook Seo
Clin Exp Pediatr. 1982;25(12):1285-1288.   Published online December 31, 1982
A case of Aicardi’s syndrome is experienced at the Department of Pediatrics, College of Medicine, Yonsei University recently. This patient was 50 days of female infant, who had infantile spasm, and her development was deteriorated recently. Her CT scan showed partial absence of corpus callosum and whose EEG was a pattern of modified hypsarrhythmia limited only on left hmisphere. She also had hemivertebra at...
Original Article
Clinical Study of Epilepsy in Children.
C J Coe, D K Han, K Y Lee, B S Kim
Clin Exp Pediatr. 1982;25(12):1234-1242.   Published online December 31, 1982
From November 1980 to June 1982, for 19 months, 636 cases of child epileptic patients were clinically investigated at Pediatric department of Yonsei Medical school, and obtained follo- wing results. 1. The epileptic patients was 4.4% of all the pediatric patients, visited or hospitalized during the same period of time. 2. Epilepsy was commoner in male child compare to female representing male to female ratio, 1.3:1. 3. The most common...
Case Report
A Case of Potter Syndrome.
Young Mi Hong, Hae Seung Kim, Jung Gon Kim, Keun Lee
Clin Exp Pediatr. 1982;25(11):1181-1184.   Published online November 30, 1982
In 1946 Potter described a series of 20 cases in infants in whom bilateral absence of the kidneys was associated with, hypoplasia of the lung and characteristic face. The main facial features she described were increased space between the eyes, a prominent fold which arises at inner canthus and sweeps downward and laterally below the eyes, unusual flattening of the nose, excessive recession of...
Original Article
Neurobehavioral Response of Newborn Infants Following Delivery by Normal Labor and Cesarean Section under General and Spinal Anesthesia.
Eun Ai Lee, Jung Hee Park, Yoon Ju Choi, Seung Ju Lee, Keun Lee
Clin Exp Pediatr. 1982;25(10):1032-1038.   Published online October 31, 1982
Scanlon*s Early Neonatal Neurobehavioral Scale was administered to 110 babies delivered by normal labor and cesarean section. Fifty of the mothers had normal vaginal delivery, thirty of the mothers were induced into general anesthesia with thiopental sodium and thirty of the mothers received spinal anesthe- sia with tetracaine before cesarean section. The Scanlon*s scale involves an assessment of the infant*s state of wekefulness, varius reflexes, his...
Case Report
A Case of Acute Fulminant Hepatitis Induced by Herpesvirus Hominus.
Hee Jung Chung, Ki Sup Chung, Duk Jin Yun, Jung Sook Kim
Clin Exp Pediatr. 1982;25(6):616-621.   Published online June 30, 1982
We have experienced a case with acute fulminant hepatitis induced by Herpesvirus homin-us. The patient, 11day-old male baby, was admitted with the chief complaints of poor sucking and jaundice for 3 days duration. On adimission, we performed bacterial cultures, liver function tests, blood coagulation test, TORCH study and routine hematologic studies. During these studies, bleeding tendency was n-oticed at the...
A Case of Cryptococcosis with Cutaneous Manifestation.
Jae Phil Kim, Hyun Ju Oh, Hyung Suk Byun, Kyung Ryong Huh, Chull Sohn
Clin Exp Pediatr. 1981;24(8):777-781.   Published online August 15, 1981
We experienced a case of cryptococcosis in a 13-year-old female who had been admitted to our hospital because of intermittent high fever and generalized lymphadenopathy accompanied by multiple nodular eruptions with erosions on the face, scalp, neck and back. The patient was treated under the impression of tuberculous lymphadenitis without any improvement. A surgical biopsy of the lymph node and...
A Case of Rt. Renal Agenesis Combined with Cryptorchism and Neuroblastoma.
Hee Jung Chung, Chul Lee, Pyung Kill Kim, Chang Jin Kim, Kwang Kill Lee, Yu Bok Lee, Ki Keun Oh
Clin Exp Pediatr. 1981;24(7):677-684.   Published online July 15, 1981
Congenital unilateral renal agenesis is a rare congenital anomaly. Furthermore, renal agenesis associated with neuroblastoma and cryptorchism is more rare in incidence. Recently we experieced a case of Rt. renal agenesis combined with cryptorchism and neuroblastoma. We diagnosed it with IVP and selective renal angiography and confirmed it with explolaparotomy and biopsy. We reviewed the literatures on renal agenesis, cryptorchism...
A Case of Congenital Generalized Lipodystrophy.
Woon Sik Kim, Kye Tae Kim, Don Hee Ahn, Keun Chan Sohn
Clin Exp Pediatr. 1981;24(2):173-180.   Published online February 15, 1981
A 4 year and 2 months old girl with peculiar appearance and abdominal protuberance was prese-nted. She was the 2nd full term product of a healthy, 37-year-old mother. Any history of neonatal problems couldn’t be elicited. At 1 month of age his mother began to notice loss of subcutaneous fat with prominent musculature. At 2 months of age he was...