A Case of Potter Syndrome Type I. |
Jong Cheol Ryu1, Jae Kwang Hong1, Jun Taek Park1, Jung Sik Min1, Chang Jee Choi1, Je Geun Chi2 |
1Department of Pediatrics, Seoul Adventist Hospital 2Department of Pathology, Seoul National University |
Potter Syndrome (type I) 1 례 |
류종철1, 홍재광1, 박준택1, 민정식1, 최창희1, 지제근2 |
1서울위생병원 소아과 2서울대학교 의과대학 병리학교실 |
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Abstract |
We have experienced a case of Potter syndrome type I in a newborn infant who presented with severe
respiratory distress soon after birth. The diagnosis was made with autopsy findings consisted of bilateral
polycystic renal dysplasia, bilateral hypoplastic lung , facies renalis, fibrocystic change of liver, patent ductus arteriosus, patent foramen ovale, ureter and urinary bladder hypoplasia and calcaneovarus.
Brief reviews of the related literatures are given.
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Key Words:
Potter syndrome type I, Facies renalis, Hypoplastic lung, Polycystic renal dysplasia. |
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