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Case Report
A case of Finnish Type of Congenital Nephrotic Syndrome.
Jeong Sik Min, Yang Kook Shon, Soo Woong Lee, Suk Chul Kang, Yong Koo Park, Moon Ho Yang
Clin Exp Pediatr. 1982;25(2):175-182.   Published online February 28, 1982
The Finnish type of Congenital Nephrotic Syndrome is characterized by large placenta, early manifestation, growth and developmental delay and resistance to treatment. Authors experienced a case of characteristic Finnish type of Congenital Nephrotic Syndrome in a girl, who was admitted to the Pediatric Department of KHUH at 2 1/1 months of age because of generalized edema and abdominal distension and...
Congenital Generalized Cytomegalic Inclusion Disease.
Byung Yun Chung, Jun Ho Kim, Go Chang Kim, Won Jae Park
Clin Exp Pediatr. 1981;24(12):1197-1202.   Published online December 15, 1981
We experienced a case of congenital cytomegalic inclusion disease. A 2100 gm female infant was born after 38 weeks gestation to a 26 years old gravida 1 para 0 abortus 0 mother. On 2nd hospital day, jaundice appeared, thereafter exchange transfuion was done for 3 times through umbilical vein. On 27 th hospital day, cardiac arrest developed suddenly and resuscitation...
Two Cases of the Salts Losing Congenital Adrenal Hyperplasia.
Hee Ju Kim, Hyung Ro Moon
Clin Exp Pediatr. 1981;24(11):1092-1099.   Published online November 15, 1981
The authers experienced two cases of salt losing congenital adrenal hyperplasia. Case I was a 100 day old male infant, who had dehydration, failure to thrive, and diffusely pigmented skin. Very low plasma aldosterone and markedly increased urinary 17KS were observed. He had been, treated with daily DOCA injection and oral hydrocortisone, successfully. Case H was a 5 year and...
A Case of Harlequin Fetus.
Eun Hee Bak, Ai Sunn Choi, Elizabeth M Nicholson, Young Shin Kwark, Jung Hee Lee
Clin Exp Pediatr. 1981;24(10):1009-1013.   Published online October 15, 1981
The Harlequin fetus-ichthyosis fetalis-is known to be rare. Recently, we experienced a case of Harlequin fetus in stillborn infant due to autosomal recessive inheritance likely. A review of literature was done briefly.
Congenital Systemic Cytomegalic Inclusion Disease: An Autopsy Case Report.
Seung Bok Cho, Boc Lyul Park, Mi Na Lee, Hea Soo Koo, Je Geun Chi
Clin Exp Pediatr. 1981;24(9):865-871.   Published online September 15, 1981
A case of systemic cytomegalovirus infection in a newborn baby is reported. This female baby was born after 36 weeks gestation to a 30 year-old mother who had no prenatal problem except for breech presentation and placenta previa for which Caesarian section was given. The mother has two healthy children. The clinical course of this baby was characterized by repeat...
Original Article
Chromosome Study of the Congenital Anomaly and Mental Retardation in Korean Children.
Ra Lee, In Joon Seol, Woo Gill Lee, Soo Jee Moon, Chong Moo Park
Clin Exp Pediatr. 1981;24(9):812-819.   Published online September 15, 1981
The authors studie 111 cases of congenital anomalies and/or mental retardation. 56cases of congenital anomalies and/or mental retardations were cared and admitted at pediatric department in Han Yang University hospital. 55 cases were in institution for the mentally retarded. The authors studied chromosome analysis about 111 cases with congenital anomalies and/or mental retardation. The results obtained were as follows: A)...
Case Report
A Case of Congenital Choledochal Cyst.
Joon Ho Kim, Jung Ju Kim, Ko Chang Kim, Byung Yun Cheong, Won Jae Park
Clin Exp Pediatr. 1981;24(6):584-588.   Published online June 15, 1981
We experienced a case of congenital choledochal cyst in a 6 months old korean female infant with complaints of abdominal distension, jaundice, loose stool and a large mass of the abdomenin the right upper quadrant since about 3 months prior to admission. The diagnosis was confirmed by clinical symptoms and signs, physical examination, radiological findings and surgical findings. She was...
A Case of Congenital Hepatic Fibrosis.
Son Moon Shin, Sang Il Lee, Joong Gon Kim, Hyo Seop Ahn, Hyung Ro Moon, Kwang Wook Ko, Je Geun Chi
Clin Exp Pediatr. 1981;24(6):577-583.   Published online June 15, 1981
Congenital hepatic fibrosis is a relatively rare liver disease in children and young adults,that is characterized by stony hard hepatomegaly and portal hypertension with relative preservation of liver function and underlying architecture. Since this Condition was first delineated by Kerr et al in 1961, approximately over 150 cases have been reported in the literature. However, congenital hepatic fibrosis was not...
Caroli's Disease.
Jong Hoon Park, In Hyun Cho, Sun Ja Lee, Dong Hyuk Kum, Soo Dong Pai
Clin Exp Pediatr. 1981;24(4):401-406.   Published online April 15, 1981
Caroli*s disease, a rare syndrome characterized by congenital, segmental saccular dilatation of intrahepatic bile ducts, is first described by Caroli & associaties in 1958. It is though by many to be part of spectrum of congenital hepatic fibrosis. The disease usually presents with bile stasis and stone formation with further complication arising from recurrent cholangitis and liver abscess. The preoperative diagnosis...
Original Article
The Clinical Study on 100 Cases of Congenital Syphillis.
Jheog Hee Hahn, Ok Sung Chung, Mi Seon Lee, Young Shin Kwark, Mi Seon Kim
Clin Exp Pediatr. 1981;24(4):329-335.   Published online April 15, 1981
The authors studied 100 cases of congenital syphilis in the newborn treated at II Sin. Women* s Hospital from 1st August 1978 to 31st July 1979. 71 infants were born in the hospital and 29 were admitted from the out patient department. The results were as follows 1.The incidence of congenital syphilis was 1% of live born deliveries. 2. Incidence of...
Case Report
Fanconi Anemia.
Sang Il Lee, Young Yul Koh, Jung Gi Suh, Hyo Seop Ahn, Chang Yee Hong
Clin Exp Pediatr. 1981;24(2):153-163.   Published online February 15, 1981
Five cases of Fanconi anemia were observed during these 7 *years. It acounts for about 6.7% of the total 75 aplastic anemia seen during those same period in SNUH. Three were boys and two were girls. The initial symptom was nasal bleeding or pallor which observed between the age of 2 years and 6 years. They all revealed growth retardation...
A case of Congenital Syphilitic Nephrotic Syndrome.
H S Kim, S K Park, D H Shin
Clin Exp Pediatr. 1981;24(1):94-99.   Published online January 15, 1981
We have experienced a case of congenital syphilitic nephrotic syndrome in a 4 months old boy, who was admitted to presbyterian hospital, Daegu, Korea. He was sucessfully treated with penicillin of 2 weeks duration. We made brief review of the related literatures.
Congenital Lobar Emphysema.
Jin Tae Kim, Ki Hong Suh, Suk Chul Kang, Chang Il Ahn
Clin Exp Pediatr. 1981;24(1):85-87.   Published online January 15, 1981
Congenital lobar emphysema is characterized by overdistension and air trapping in the affected lobe, concomitant compression of remaining long tissue, displacement of the mediastinum by herniation of the emphysematons lobe across the anterior mediastinum into the opposite chest. The occurrence of this condition early in life, its sudden appearance in the absence of infection and foreign body in the bronchus...
Original Article
A Clinicostatistical Study of Congenital Alimentary Tract Obstruction.
Sang Pok Suck, Yong Soo Youn, Han Woong Choi, Woo Ki Kim, Kwi Won Park
Clin Exp Pediatr. 1981;24(1):36-44.   Published online January 15, 1981
Clinicostatistical datsa on 314 patients with congenital alimentary tract obstruction at the Department of Pediatrics and Pediatric Surgery of Seoul National University Hospital from January, 1974 to July, 1980 are presented and reviewed. The results are as follows; 1. Congenital megacolon(133 cases) is the most common congenital alimentary tract obstruction, and anorectal malformations(127 cases), congental duodenal obstruction(20 cass), esophageal atresia(12...