College of Medicine, Yonsei University, Seoul, Korea Wilms tumor is the second most common malignant retroperitoneal tumor. Inferior vena cava and right atrial involvement is found in about 4-10% and 0.5-3% of cases, respectively. But, right ventricular involvement has not been reported. We experienced a case of Wilms tumor with right ventricular invasion in a 2 year-old male who presented intermittent... |
Purpose : To evaluate the usefulness of magnetic resonance cholangiography(MRC) for the diagnosis of biliary atresia in infantile cholestatic jaundice. Methods : Fifty consecutive infants with cholestatic jaundice underwent single-shot MRC for 3 years. The radiologic diagnosis of non-biliary atresia with MRC was based on visualization of the common bile duct and common hepatic duct. The diagnosis of biliary atresia was... |
Purpose : In recent years, the authors experienced a distinctive clinical entity of multiple intestinal ulcerations and perforations in infants. The purpose of this study was to describe the clinical characteristics of this entity, examine th possible pathogenesis and the effective treatment. Methods : Seven infants underwent abdominal exploration under suspicion of surgical abdomen and were noted to have multiple intestinal... |
Choledochal cysts are congenital or acquired lesions of the biliary tree with a cystic dilatation of the bile duct. We experienced a choledochal cyst accompanying acute pancreatitis caused by anomalous pancreaticobiliary ductal union(APBDU) in a 2 year old boy. The choledochal cyst associated with APBDU is rarely encountered in the clinical field, and thus we report this case with the presentation of abdominal ultrasonogram, computed... |
Arteriovenous malformation in the gastrointestinal tract is very rare in children. However, when present they are frequently a source of either acute and massive, or chronic occult hemorrhage, and may be difficult to diagnosis. In reviewing Korean literature, only 2 cases has been reported in adults. We have experienced a rare case of arteriovenous malformation in a 1 year and 10 month-old female... |
An endodermal sinus tumor of the vagina, a rare pediatric malignancy, was managed with c onservative surgey followed by adjuvant chemotherapy(vincristine, actinomycin D, cyclophosphamide : VAC). Treatment related complications were acceptible, and there is no evidence of d isease twenty months after diagnosis. As a treatment option, primary conservative surgery and adjuvant chemotherapy is viewed as a highly attractive alternative... |
Rhabdomyosarcoma is a relatively common solid tumor in infants, children and adolescents, according for 4% to 8% of malignant disease in children less than 15 years old. Use of a multimodal approach to treatment has resulted in a dramatic improvement. Yonsei Cancer Center in Korea, since it's establishment in 1975, has been a state of multimodal approach. Thirty-seven cases of childhood... |
The omphalomesenteric duct in the embryo is a communication between the yolk sac and primitive gut. The duct closes by six to eight weeks of intrauterine life and disappears soon after. Patent omphalomesenteric duct is a congenital anomaly which occurs when there is incomplete closure of the duct during this period. The authors experienced a cases whereby a 29-day old male baby had patent... |
A clinical study of 24 patients with congenital choledochal cyst who had been admitted to Severance Hospital, Yonsei University College of Medicine during the 16 year peroid from January, 1971 to December, 1986 was done. The results were as follows; 1) Of the 24 cases studied, the highest incidence of this cyst, 15 cases (62.5%), was found in children younger than 10 years of age. The... |
There are four main groups of clinical manifestations in salmonellosis, gastroenteritis。 enteric fever, localized infection, and chronic carrier state, that may occur individually, simultaneously or consecutively in the course of an infection. The authors experienced a case of salmonella gastroenteritis complicated with empyema of gall bladder in a 12-year-old male patient. The clinical diagnosis was confirmed on the operating table and... |
There are little reports on Cushing’s syndrome in children. We have seen a case of Cushing’s syndrome due to left adrenal adenoma from 5 year 6 months old girl. She has been complained from obesity with, buffalo hump, hirsutism and vaginal spotting. Her blood cortisol levels were high and no diurnal variation. No suppression was occurred following dexamethasone 1 mg overnight or 4 mg... |
Malformation of the anus and rectum, frequently refered to as imperforate anus are the most common of congenital anomalies among the congenital anomalies of gastrointestinal tract, occuring about once in every 5,000births. They consist of variety of lesions ranging from mild congenital stenosis of the anus which requires simple dilation for cure to complex deformities which present some of the... |
Authors experienced a case of cavernous hemangioma attached to the falciform ligament of the liver in a 9 years and 2 months old boy. It seems to be the first case reported in the literature. The review of literature was made briefly. |
A 2 month old male infant was admitted to Severance hospital due to bile stained vomiting; and abdominal distention for 2 days via emergency room. On physical examination, acutely ill appearance with lethargy, subnormal temperature, sunken fontanel, dry mouth, coated tongue, abdominal distention, and absent bowel sounds were noted and clinical impression could not be ruled out paralytic ileus due... |
Intussusception is most frepuent and important surgical condition in infancy and chilchood. This clinical studies consist of 210 cases who were admitted to the department of pediatrics and surgery of Severance Hospital from Jan. 1957 to Dec. 1971. 1) In age incidency, 68. 8% of the patients are under one year of age. The peak incidence occurs from 4th to 9th month. 2) Males... |
Intussusception in Henoch-Schoenlein purpura is of interest because of its rarity and the importance of making what may be a difficult diagnosis. In the world literature there were less than 40 cases of intussusception in Henoch-Schoenlein purpura up to 1962 by Grossman et al. Our patient seems to be the first case in Korea. We presented a case of intussusception... |