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Congenital hepatic fibrosis is a relatively rare disease of liver in children and young adults,
manifesting a heredofamilial tendency, that is characterized by hepatosplenomegaly, protal hypertension
and frequent renal involvement. A generalized portal and interlobular fibrosis of liver are
characteristic finding on microscopy, with relative preservation of hepatocyte and liver function.
Recently, we have experienced a case of congenital hepatic fibrosis in a... |
