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A case of histiocytosis X (Hand-Schuller-Christian syndrome) in a 3 year old girl is presented.
The patients has the triad of exophthalmos, diabetes insipidus and skeletal lesions, plus hepatomegaly,
wide spread pulmonary infiltration and growth retardation.
The patient was treated with chlorambucil, prednisone, radiation therapy and
chlorpropamide therapy for diabetes insipidus with good response.
Similar cases reported in literature are briefly... |