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Case Report
A Case of Histiocytosis X(Hand-Schuller-Christian Syndrome).
Yeong Bong Park, Jin Heon Kim, Jong Myeon Hong, Chang Soo Ra
Clin Exp Pediatr. 1983;26(12):1209-1214.   Published online December 31, 1983
A case of histiocytosis X (Hand-Schuller-Christian syndrome) in a 3 year old girl is presented. The patients has the triad of exophthalmos, diabetes insipidus and skeletal lesions, plus hepatomegaly, wide spread pulmonary infiltration and growth retardation. The patient was treated with chlorambucil, prednisone, radiation therapy and chlorpropamide therapy for diabetes insipidus with good response. Similar cases reported in literature are briefly...
Nephrogenic Diabetes Insipidus occurred in 2 Brother.
Jin Heon Kim, Cheol Won Park, Bong Soo Lee, Chang Soo Ra
Clin Exp Pediatr. 1983;26(9):916-921.   Published online September 30, 1983
Nephrogenic diabetes insipidus is a congenital hereditary disorders in which the kidney do not respond to vasopressin, and the disease occurs principally in males and is probably inherited by Xlinked recessive mode. We experienced two cases of nephrogenic diabetes insipidus occurred in brothers. The clinical manifestations were extreme thirst and frequent urination of large volume of dilute urine, approximately 5,500ml per day with specific gravity...
A Case of Hand Schuller Christian Disease.
Yeon Saeng Lee, Soo Young Kim, So Kyung Park, Dong Hak Shin
Clin Exp Pediatr. 1983;26(4):392-396.   Published online April 30, 1983
Hand-Schuller-Christian disease is reactive granulomatous lesion with histiocytic proliferation, the cause of which is unknown. Recently, we experienced a case in a 3 years old female with polydipsia and polyuria. We established the diagnosis with clinical features, radiologic examination and bone biopsy- Histiologic examination of frontal bone showed mild to moderate infiltration of eosinophils， lymphocytes, plasma cells and large histioytes and fibrosis. Similiar cases reported in...