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Malignant atrophic papulosis (Degos’ disease) is characterized by porcelain-white skin lesions. It
has unknown etiology and bad prognosis. Death usually occurs from multiple intestinal perforations
weeks to years after onset.
We experienced a case of Degos’ disease in a 12-year-old male patient who had porcelain white
papules on face, trunk and extremities. Histopathologic studies showed broad epidermal necrobiosis
with thrombotic arteriolar occlusion.
A brief review of... |