• Search
  • Advanced Search

Search

  • HOME
  • Search
Original Article
A case of Dandy-Walker syndrome.
Kyung Hee Kim, Jong Leam Choi, Hyo Sook Hong, Wan Seop Kim
Clin Exp Pediatr. 1989;32(11):1586-1591.   Published online November 30, 1989
Dandy-Walker syndrome is a developmental disorder of the brain associated with hydrocephalus, possterior fossa cyst and maldevelopment of the cerebellar vermis and is a result of outlet obstruction of the fourth ventricle. We experienced a case of a 6 day old male neonate who presented macrocephaly which revealed marked dilated fourth & lateral ventricle, large posterior fossa cyst and hypoplastic cerebellum, no vermis on Brain...
A Case of Cockayne Syndrome.
Jong Leam Choi, Kyung Hee Kim, Hyo Sook Hong, Wan Soeb Kim
Clin Exp Pediatr. 1989;32(10):1422-1427.   Published online October 31, 1989
We experienced a case of Cockayne syndrome in a 12 10/12 year-old male who had characteristic manifestations with cachectic dwarfism, severe mental retardation, intracranial calcifications, an unusal face, photo-sensitive dermatitis and joint flexion contractures. Laboratory investigations have not revealed any consistent abnormality. We report this case with brief review of some related literatures.
A Case of Recurrent Bacterial Meningitis due to Congenital Cribriform Plate Defect.
Hong Chul Lee, Jong Leam Choi, Wan Soeb Kim, Myung Ho Lee
Clin Exp Pediatr. 1989;32(3):412-417.   Published online March 31, 1989
One patient with a history of recurrent bacterial meningitis was examined with skull and sinus radiographs, routine cranial computed tomography and immunologic evaluation. None of these studies were diagnostic. Thin-section (1-2 mm) direct coronal computed cranial tomography demonstrated congenital cribriform plate defect. This patient was repaired surgically and no further meningitis has developed for 16 months