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Original Article
A case of Dandy-Walker syndrome.
Kyung Hee Kim, Jong Leam Choi, Hyo Sook Hong, Wan Seop Kim
Clin Exp Pediatr. 1989;32(11):1586-1591.   Published online November 30, 1989
Dandy-Walker syndrome is a developmental disorder of the brain associated with hydrocephalus, possterior fossa cyst and maldevelopment of the cerebellar vermis and is a result of outlet obstruction of the fourth ventricle. We experienced a case of a 6 day old male neonate who presented macrocephaly which revealed marked dilated fourth & lateral ventricle, large posterior fossa cyst and hypoplastic cerebellum, no vermis on Brain...
A Case of Cockayne Syndrome.
Jong Leam Choi, Kyung Hee Kim, Hyo Sook Hong, Wan Soeb Kim
Clin Exp Pediatr. 1989;32(10):1422-1427.   Published online October 31, 1989
We experienced a case of Cockayne syndrome in a 12 10/12 year-old male who had characteristic manifestations with cachectic dwarfism, severe mental retardation, intracranial calcifications, an unusal face, photo-sensitive dermatitis and joint flexion contractures. Laboratory investigations have not revealed any consistent abnormality. We report this case with brief review of some related literatures.
Clinical Bacteriologic Study of Serratia Marcescens Septicemia.
Hyo Sook Hong, Wan Seob Kim, Oh Kyung Lee, Myung Ho Lee
Clin Exp Pediatr. 1987;30(12):1409-1418.   Published online December 31, 1987
We experienced an outbreak of Serratia marcescens septicemia during a 2-month-10-day period (Apirl the 10th, 1985-June the 6th, 1985) in the Chonju Presbyterian medical center, pediatric ward. The clinical and bacteriological features of 22 patients with septicemia were described. There were 25 bacterial isolates from 22 patients. Twenty cases of 22 patients recovered, while 2 patients died, both premature infants. This indicated the seriousness...
Case Report
A Case of Beckwith-Wiedemann Syndrome.
Hyo Sook Hong, Hong Chul Lee, Oh Kyung Lee, Myung Ho Lee
Clin Exp Pediatr. 1987;30(10):1166-1169.   Published online October 31, 1987
Beckwith-Wiedemann syndrome constitutes a clinicopathologic entity characterized macroglossia, omphalocele or umblical hernia, visceromegaly, postnatal gigantism, microcephaly, Nevus flammeus, ear lobe grooves, hemihypertrophy and other abnormalities. The anomalies of the syndrome are facultative and not obligatory. We experience one case of Beck with-Wiedemann syndrome. This 1-day-aged female neonate showed macroglossia, gigantism, omphalocele and hypoglycemia. Review of literature was done briefly.